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KMID : 1144720210250040332
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Investigative Magnetic Resonance Imaging
2021 Volume.25 No. 4 p.332 ~ p.337
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Cardiac Behcet's Disease Presenting with Right Ventricular Endomyocardial Fibrosis and Intracardiac Thrombosis: a Case Report
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Choi Eun-Ji
Kim Min-Sun
Koo Hyun-Jung
Song Jae-Kwan
Song Joo-Seon
Kang Joon-Won
Yang Dong-Hyun
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Abstract
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Behcet’s disease is a chronic inflammatory disorder involving vessels of various sizes and organs, including the skin, joints, gastrointestinal tract, lungs, and cardiovascular system. The etiology of Behcet’s disease is unclear, and clinical diagnosis is important in the absence of definitive laboratory or pathological findings diagnostic of Behcet’s disease. Cardiac involvement is rare but might present as endocarditis, myocarditis, pericarditis, or intracardiac thrombosis. This report presents a case of Behcet’s disease involving the heart in a 22-year-old man with unusual manifestations of right ventricular fibrosis and intracardiac thrombosis. Cardiac magnetic resonance imaging revealed multiple intracardiac thrombi and delayed diffuse subendocardial enhancement involving the right ventricle. No peripheral eosinophilia was detected. Endomyocardial biopsy showed mixed inflammatory cell infiltrates. Based on the patient’s clinical history of oral ulcer and arthritis, a diagnosis of Behcet’s disease was made considering the clinical, radiological, and histological findings. Intracardiac thrombi and endomyocardial fibrosis are rare manifestations of Behcet’s disease, and the diagnosis is often a clinical challenge. Early diagnosis is important for appropriate management. Behcet’s disease should be considered in the differential diagnosis of patients with intracardiac thrombosis and endomyocardial fibrosis of the right chamber.
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KEYWORD
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Behcet’s disease, Intracardiac thrombosis, Endomyocardial fibrosis, Magnetic resonance imaging
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